{"id":37025,"date":"2026-04-11T09:00:12","date_gmt":"2026-04-11T00:00:12","guid":{"rendered":"https:\/\/blog.agentsoft.co.kr\/index.php\/2026\/04\/11\/37025\/"},"modified":"2026-04-11T09:00:12","modified_gmt":"2026-04-11T00:00:12","slug":"%ea%b0%88%eb%9d%bd%ed%86%a0%ec%8a%a4%ed%98%88%ec%a6%9dgalactosemia-%ea%b0%84%ed%98%b8%ec%a7%84%eb%8b%a8-%eb%b0%8f-%eb%aa%a9%ed%91%9c-%ec%a4%91%ec%9e%ac-6%ea%b0%80%ec%a7%80","status":"publish","type":"post","link":"https:\/\/blog.agentsoft.co.kr\/index.php\/2026\/04\/11\/37025\/","title":{"rendered":"\uac08\ub77d\ud1a0\uc2a4\ud608\uc99d(Galactosemia) \uac04\ud638\uc9c4\ub2e8 \ubc0f \ubaa9\ud45c, \uc911\uc7ac 6\uac00\uc9c0"},"content":{"rendered":"<p><img decoding=\"async\" src=\"https:\/\/image4.happycampus.com\/Production\/thumbnail\/2024\/05\/23\/data29912429-0001.jpg\"><img decoding=\"async\" src=\"https:\/\/image4.happycampus.com\/Production\/thumbnail\/2024\/05\/23\/data29912429-0002.jpg\"><\/p>\n<p><strong>\ubaa9\ucc28<\/strong><\/p>\n<p>1. \uac08\ub77d\ud1a0\uc2a4\ud608\uc99d(Galactosemia) \ubb38\ud5cc\uace0\ucc30<br \/>\n2. \uac08\ub77d\ud1a0\uc2a4\ud608\uc99d(Galactosemia) \uac04\ud638\uc9c4\ub2e8 \ubc0f \uc911\uc7ac \ub808\ud3ec\ud2b8<\/p>\n<p><strong>\ubcf8\ubb38\ub0b4\uc6a9<\/strong><\/p>\n<p>*\uac1c\uc694<br \/>\n\uac08\ub77d\ud1a0\uc2a4\ud608\uc99d(Galactosemia)\uc740 \uc720\uc804\uc801\uc73c\ub85c \uc720\uc804\ub418\ub294 \ub300\uc0ac \uc9c8\ud658\uc73c\ub85c, \uac08\ub77d\ud1a0\uc2a4(Galactose)\ub97c \uae00\ub8e8\ucf54\uc2a4(Glucose)\ub85c \uc804\ud658\ud558\ub294 \ub370 \ud544\uc694\ud55c \ud6a8\uc18c\uac00 \uacb0\ud54d\ub418\uc5b4 \ubc1c\uc0dd\ud569\ub2c8\ub2e4. \uc774\ub85c \uc778\ud574 \uac08\ub77d\ud1a0\uc2a4\uc640 \uadf8 \ub300\uc0ac\uc0b0\ubb3c\uc774 \uccb4\ub0b4\uc5d0 \ucd95\uc801\ub418\uc5b4 \ub3c5\uc131\uc744 \uc720\ubc1c\ud569\ub2c8\ub2e4. \uc774 \uc9c8\ud658\uc740 \uc2e0\uc0dd\uc544 \uc120\ubcc4 \uac80\uc0ac\ub85c \uc870\uae30 \ubc1c\uacac\ub420 \uc218 \uc788\uc73c\uba70, \uc870\uae30 \uc9c4\ub2e8\uacfc \uc801\uc808\ud55c \uce58\ub8cc\uac00 \ud544\uc218\uc801\uc785\ub2c8\ub2e4.<\/p>\n<p>*\ubcd1\ud0dc\uc0dd\ub9ac<br \/>\n\uac08\ub77d\ud1a0\uc2a4\ud608\uc99d\uc740 \uc8fc\ub85c \uc138 \uac00\uc9c0 \ud615\ud0dc\ub85c \ub098\ub20c \uc218 \uc788\uc2b5\ub2c8\ub2e4:<\/p>\n<p>1. \ud074\ub798\uc2dd \uac08\ub77d\ud1a0\uc2a4\ud608\uc99d(Classic Galactosemia): \uac00\uc7a5 \ud754\ud558\uace0 \uc2ec\uac01\ud55c \ud615\ud0dc\ub85c, \uac08\ub77d\ud1a0\uc2a4-1-\uc778\uc0b0 \uc720\ub9ac\ub51c\ud2b8\ub79c\uc2a4\ud37c\ub77c\uc81c(GALT) \ud6a8\uc18c\uc758 \uacb0\ud54d\uc73c\ub85c \uc778\ud574 \ubc1c\uc0dd\ud569\ub2c8\ub2e4. \uc774 \ud6a8\uc18c\ub294 \uac08\ub77d\ud1a0\uc2a4-1-\uc778\uc0b0\uc744 UDP-\uac08\ub77d\ud1a0\uc2a4(UDP-Galactose)\ub85c \uc804\ud658\ud558\ub294 \uc5ed\ud560\uc744 \ud569\ub2c8\ub2e4.<br \/>\n2. \uac08\ub77d\ud1a0\ud0a4\ub098\uc81c \uacb0\ud54d(Galactokinase Deficiency): \uac08\ub77d\ud1a0\ud0a4\ub098\uc81c(GALK) \ud6a8\uc18c\uc758 \uacb0\ud54d\uc73c\ub85c \ubc1c\uc0dd\ud558\uba70, \uc8fc\ub85c \ubc31\ub0b4\uc7a5\uc744 \uc720\ubc1c\ud569\ub2c8\ub2e4.<br \/>\n3. UDP-\uac08\ub77d\ud1a0\uc2a4-4-\uc5d0\ud53c\uba38\ub77c\uc81c \uacb0\ud54d(UDP-galactose-4-epimerase deficiency): \uc774 \ud6a8\uc18c\uc758 \uacb0\ud54d\uc740 \ub9e4\uc6b0 \ub4dc\ubb3c\uba70, \ub2e4\uc591\ud55c \uc784\uc0c1 \uc99d\uc0c1\uc744 \ub098\ud0c0\ub0bc \uc218 \uc788\uc2b5\ub2c8\ub2e4.<\/p>\n<p>*\uc5ed\ud559<br \/>\n\uac08\ub77d\ud1a0\uc2a4\ud608\uc99d\uc740 \uc804 \uc138\uacc4\uc801\uc73c\ub85c \ubc1c\uc0dd\ud558\uba70, \uadf8 \ube48\ub3c4\ub294 \uc778\uad6c\uc9d1\ub2e8\uc5d0 \ub530\ub77c \ub2e4\ub985\ub2c8\ub2e4. \uc77c\ubc18\uc801\uc73c\ub85c 30,000\uba85\uc5d0\uc11c 60,000\uba85 \uc911 1\uba85\uc758 \uc2e0\uc0dd\uc544\uac00 \uc601\ud5a5\uc744 \ubc1b\uc2b5\ub2c8\ub2e4. \uc720\uc804\uc801 \uc694\uc778\uc5d0 \uc758\ud574 \uc0c1\uc5fc\uc0c9\uccb4 \uc5f4\uc131\uc73c\ub85c \uc720\uc804\ub429\ub2c8\ub2e4.<br \/>\n\uc784\uc0c1 \uc99d\uc0c1<br \/>\n\uac08\ub77d\ud1a0\uc2a4\ud608\uc99d\uc758 \uc784\uc0c1 \uc99d\uc0c1\uc740 \uc8fc\ub85c \uc2e0\uc0dd\uc544\uae30\uc640 \uc720\uc544\uae30\uc5d0 \ub098\ud0c0\ub0a9\ub2c8\ub2e4. \uc8fc\uc694 \uc99d\uc0c1\uc740 \ub2e4\uc74c\uacfc \uac19\uc2b5\ub2c8\ub2e4:<\/p>\n<p>\u2022 \ud669\ub2ec(Jaundice): \uac04 \uae30\ub2a5 \uc774\uc0c1\uc73c\ub85c \uc778\ud55c \ud669\ub2ec\uc774 \ubc1c\uc0dd\ud560 \uc218 \uc788\uc2b5\ub2c8\ub2e4.<br \/>\n\u2022 \uad6c\ud1a0(Vomiting): \uac08\ub77d\ud1a0\uc2a4 \uc12d\ucde8 \ud6c4 \uad6c\ud1a0\uac00 \ube48\ubc88\ud558\uac8c \ubc1c\uc0dd\ud569\ub2c8\ub2e4.<br \/>\n\u2022 \uac04 \ube44\ub300(Hepatomegaly): \uac04\uc774 \ube44\ub300\ud574\uc9c0\uace0 \uae30\ub2a5\uc774 \uc800\ud558\ub429\ub2c8\ub2e4.<br \/>\n\u2022 \ubc31\ub0b4\uc7a5(Cataracts): \ub208\uc758 \uc218\uc815\uccb4\uc5d0 \ubc31\ub0b4\uc7a5\uc774 \uc0dd\uae38 \uc218 \uc788\uc2b5\ub2c8\ub2e4.<br \/>\n\u2022 \uc131\uc7a5 \uc9c0\uc5f0(Growth Failure): \uc131\uc7a5\uacfc \ubc1c\ub2ec\uc774 \uc9c0\uc5f0\ub429\ub2c8\ub2e4.<br \/>\n\u2022 \uc800\ud608\ub2f9\uc99d(Hypoglycemia): \ud608\ub2f9 \uc218\uce58\uac00 \ub0ae\uc544\uc9c8 \uc218 \uc788\uc2b5\ub2c8\ub2e4.<br \/>\n\u2022 \uc2e0\uacbd\uacc4 \uc774\uc0c1(Neurological Symptoms): \uc2ec\ud55c \uacbd\uc6b0 \ub1cc \uc190\uc0c1\uacfc \ubc1c\ub2ec \uc9c0\uc5f0\uc774 \ubc1c\uc0dd\ud560 \uc218 \uc788\uc2b5\ub2c8\ub2e4.<\/p>\n<p>\ucd9c\ucc98 : <a href=\"https:\/\/www.happycampus.com\/report-doc\/29912429\/\" target=\"_blank\">\ud574\ud53c\ucea0\ud37c\uc2a4<\/a><\/p>\n","protected":false},"excerpt":{"rendered":"<p>\ubaa9\ucc28 1. \uac08\ub77d\ud1a0\uc2a4\ud608\uc99d(Galactosemia) \ubb38\ud5cc\uace0\ucc30 2. \uac08\ub77d\ud1a0\uc2a4\ud608\uc99d(Galactosemia) \uac04\ud638\uc9c4\ub2e8 \ubc0f \uc911\uc7ac \ub808\ud3ec\ud2b8 \ubcf8\ubb38\ub0b4\uc6a9 *\uac1c\uc694 \uac08\ub77d\ud1a0\uc2a4\ud608\uc99d(Galactosemia)\uc740 \uc720\uc804\uc801\uc73c\ub85c \uc720\uc804\ub418\ub294 \ub300\uc0ac \uc9c8\ud658\uc73c\ub85c, \uac08\ub77d\ud1a0\uc2a4(Galactose)\ub97c \uae00\ub8e8\ucf54\uc2a4(Glucose)\ub85c \uc804\ud658\ud558\ub294 \ub370 \ud544\uc694\ud55c \ud6a8\uc18c\uac00 \uacb0\ud54d\ub418\uc5b4 \ubc1c\uc0dd\ud569\ub2c8\ub2e4. \uc774\ub85c \uc778\ud574 \uac08\ub77d\ud1a0\uc2a4\uc640 \uadf8 \ub300\uc0ac\uc0b0\ubb3c\uc774 \uccb4\ub0b4\uc5d0 \ucd95\uc801\ub418\uc5b4 \ub3c5\uc131\uc744 \uc720\ubc1c\ud569\ub2c8\ub2e4. \uc774 \uc9c8\ud658\uc740 \uc2e0\uc0dd\uc544 \uc120\ubcc4 \uac80\uc0ac\ub85c \uc870\uae30 \ubc1c\uacac\ub420 \uc218 \uc788\uc73c\uba70, \uc870\uae30 \uc9c4\ub2e8\uacfc \uc801\uc808\ud55c \uce58\ub8cc\uac00 \ud544\uc218\uc801\uc785\ub2c8\ub2e4. *\ubcd1\ud0dc\uc0dd\ub9ac \uac08\ub77d\ud1a0\uc2a4\ud608\uc99d\uc740 \uc8fc\ub85c \uc138 \uac00\uc9c0 \ud615\ud0dc\ub85c \ub098\ub20c [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[1],"tags":[9301,32483],"class_list":["post-37025","post","type-post","status-publish","format-standard","hentry","category-uncategorized","tag-__aa","tag-a"],"_links":{"self":[{"href":"https:\/\/blog.agentsoft.co.kr\/index.php\/wp-json\/wp\/v2\/posts\/37025","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/blog.agentsoft.co.kr\/index.php\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/blog.agentsoft.co.kr\/index.php\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/blog.agentsoft.co.kr\/index.php\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/blog.agentsoft.co.kr\/index.php\/wp-json\/wp\/v2\/comments?post=37025"}],"version-history":[{"count":0,"href":"https:\/\/blog.agentsoft.co.kr\/index.php\/wp-json\/wp\/v2\/posts\/37025\/revisions"}],"wp:attachment":[{"href":"https:\/\/blog.agentsoft.co.kr\/index.php\/wp-json\/wp\/v2\/media?parent=37025"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/blog.agentsoft.co.kr\/index.php\/wp-json\/wp\/v2\/categories?post=37025"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/blog.agentsoft.co.kr\/index.php\/wp-json\/wp\/v2\/tags?post=37025"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}